Endometriosis is presence of ectopic endometrial tissue outside uterine cavity. Although it is rare, foci of endometrial tissue can present in extra pelvic sites such as umbilicus, lungs, abdominal surgical scars and bowel. Umbilical endometriosis is a rare condition with an unclear pathophysiology. It is characterized by a discolored nodule in the umbilicus, which presents as cyclical menstruation symptoms like pain, swelling and bleeding. Imaging and histopathological examination can predict and confirm the diagnosis. In Nepalese literature, extra pelvic and pelvic site endometriosis have been explored, however there are no case reports of primary umbilical endometriosis. Therefore, we describe a case of a 38-year-old woman who presented with umbilical bleeding. The diagnosis of endometriosis was confirmed by clinical, radiological, and histopathological examination.